Sirenomelia, presentation of a clinical case and review of the literature.
Sirenomelia
Abstract
Sirenomelia is a rare congenital anomaly, whose main characteristic is the fusion of the lower extremities; the etiology is still unknown, however there are several theories proposed to determine the origin of this rare entity. It is difficult to diagnose prenatally, since it is usually associated with oligohydramnios. The associated malformations are very variable, but usually incompatible with life, therefore the prognosis is bleak. In the following article we report a clinical case of a newborn with sirenomelia, in the Hospital Obrero N°2 of the Caja Nacional de Salud, who due to the association of bilateral renal agenesis, presents a poor prognosis and dies at eight hours of life.
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References
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